Arrhythmogenic Right Ventricular Dysplasia Presenting with Sustained Ventricular Tachycardia: A Case Report

Arrhythmogenic right ventricular dysplasia (ARVD) is a cardiomyopathy characterized pathologically by fibrofatty tissue replacement of the myocyte of the right ventricle (RV) and clinically by life-threatening ventricular arrhythmias in young people. It is a major cause of sudden death. We present the case of a 60-year-old man with cardiovascular risk factors, was admitted for unstable ventricular tachycardia (VT) treated immediately with synchronized cardioversion. After the stabilization of the patient, Electrocardiogram demonstrated an epsilon wave in precordial leads and diffuse T-wave inversions. Transthoracic echocardiography revealed a dilated, hypokinetic right ventricle with moderately reduced function and a focal area of dyskinesia. The diagnosis of arrhythmogenic right ventricular dysplasia (ARVD) was made and an implantable cardioverter defibrillator (ICD) was indicated for secondary prevention. This case report will present the clinical presentation, diagnosis and management of this rare disease.